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Archive for March, 2014

Do what you love and your skin will follow.

As many of you affected with ichthyosis already know, at times, this condition can present enormous challenges. And yet, as many of you also know there are still other times when ichthyosis is simply a background hum to the music of life.  Member Brian Gass, affected with CIE, is living, walking, and hiking proof that although his ichthyosis is a part of his life’s journey, it follows his lead, trailing far behind his pursuit of passions, dreams, and interests.

Recently Brian contacted us to let us know he’d be doing a little traveling this summer. Well, actually a lot of traveling – 2,650 miles up the spine of the Sierras from Mexico to Canada, to be exact. Although he is an avid hiker, racking up “over a thousand trail miles on three continents,” this journey will prove to be a journey of his lifetime. And for the benefit of others affected by ichthyosis who share in his love of the outdoors, periodically throughout the summer he will be reporting back to FIRST and on his blog:   (http://hikeonthegoodfoot.blogspot.com/).  Not only will Brian be sharing an up-close view of the most breathtaking terrain, but he will be sharing everything he learns and experiences about the care and safety of his skin along the way.

We are happy to share Brian’s mission and his message: do what you love first and your skin will follow. 

Here is a personal note from Brian with more information regarding the details of his upcoming adventure.

Skin Infection in Ichthyosis

 


Dr. John Browning

 

 

 

 

 

 

John C. Browning, MD, FAAD, FAAP
Assistant Professor, Baylor College of Medicine
Chief of Dermatology, Children’s Hospital of San Antonio

 

Today, we’d like to welcome Dr. John Browning, a member of the FIRST Medical Advisory Board, and our very first Medical Guest Blogger, as he discusses signs, prevention and treatment of infection in ichthyosis.

Skin Infection in Ichthyosis

Since patients with ichthyosis have an impaired or abnormal skin barrier, they are at higher risk for certain types of infection.  In particular certain fungal infections can often hide out from the immune system while infecting areas of thickened scale in the skin. This has been reported most frequently in cases of ichthyosis vulgaris, lamellar ichthyosis, and keratitis, ichthyosis and deafness (KID) syndrome, although any type of ichthyosis with thickened scale is at higher risk.

People with ichthyosis can also be at high-risk for certain types of bacterial infection.  In particular individuals with epidermolytic ichthyosis can become colonized with staphylococcus aureus, as well as other skin pathogens. This colonization can lead to infection.

Colonization vs. Infection

Colonization refers to bacteria living on our skin for long periods of time without the onset of infection.  It can often be noted from increased irritation and maceration (wetness) of the skin with a faint odor.

Active infection occurs when a bacterial strain undergoes uncontrolled growth. When the body attempts to mount a defense against this overgrowth you begin to see the typical symptoms of infection. Infection is characterized by warm and tender skin with increased drainage.  If there is concern for a bacterial infection, a swab can be taken in the clinic, which can let you know if an infection is present.  However it takes 48 to 72 hours to have results from a bacterial culture.

Prevention

Taking dilute bleach bath by adding a half cup of bleach to a bath tub (¼ cup if tub only ¼ full, or 1 tsp per gallon) can help reduce colonization and prevent infection.  Although this sounds like a strange recommendation, bleach has been used for many years in medicine.  Unlike antibiotics, there is no risk for resistance when using bleach.  Often patients benefit from continued use of dilute bleach baths or bleach washes in order to prevent infection.  It is important to remember that the concentration of bleach in a “bleach bath” is similar to the amount of chlorine in a swimming pool. (While bleach baths are helpful in preventing bacterial skin infections, they have not been shown to prevent outer ear infections (otitis externa).  If prone to ear infections then consider adding a couple of drops of a mixture of rubbing alcohol and white vinegar 1:1, to each ear after bathing).

Is important to recognize areas of persistent drainage or pain, as well as discharge, which may be a sgn of infectio. Be sure to see your doctor who may need to start you on an oral antibiotic.  Remember: bleach baths only prevent infection but cannot treat a bacterial infection once it has occurred.

Treatment

Some patients with ichthyosis are prone to recurrent fungal infections.  These individuals may  benefit from periodically taking an oral course of a systemic antifungal agent such as terbinafine.  It is helpful to discuss this option with your doctor.  It is also important in recurrent fungal  infections to check your fingernails and toenails. Thickened fingernails and toenails could be a sign of persistent fungal infection of the nails which may be spreading to other parts of your body and leading to this infection recurrence.   In cases of a fungal infection a quick in-office scraping by the dermatologist can let you know right away whether your skin is infected.

Recognizing Scabies

Lastly, scabies is a parasitic infection where mites invade your skin.  It is characterized by increased itching and scale.  Often patients have itchy bumps on their wrists, ankles, and waist line.  In severe cases the palms and soles become thickened.  Your dermatologist can do a quick skin scraping and make this diagnosis in clinic.

It is always important if you have areas of your skin that are not healing or worsening to visit your doctor and see if any additional test should be done.